Cruveilhier-Baumgarten disease

Cruveilhier-Baumgarten disease: Description, Causes and Risk Factors:Cruveilhier-Baumgarten disease is a rare condition, characterized by the presence of prominent umbilical or paraumbilical veins, abdominal venus hum with thrill, splenomegaly, normal or small liver without evidence of cirrhosis, portal hypertension with esophageal varices and hypersplenism.Researchers identified two different clinical entities: (1) the Cruveilhier-Baumgarten disease where primary liver disease, mainly cirrhosis or portal hypertension is responsible for the extensive dilatation of the paraumbilical veins and recanalization of the umbilical vein and (2) Cruveilhier-Baumgarten disease where the clinical picture is the result of a congenitally patent umbilical vein with little demonstrable liver disease or portal tract abnormality.Cruveilhier-Baumgarten diseaseIn classic Cruveilhier-Baumgarten disease, the umbilical portion of left portal vein feeds a paraumbilical vein, which leaves the liver and then heads towards the umbilicus. The paraumbilical vein is seen as a tubular structure arising in the falciform ligament between the left lobe of liver, leading from the left portal vein to veins of the anterior abdominal wall. The development of a large re-canalized paraumbilical vein has been found to prevent formation of bleeding esophageal varices and predisposes to hepatic encephalopathy. These subcutaneous collaterals may undergo spontaneous hemorrhage or inadvertent significant bleeding during abdominal paracentesis.Symptoms:Portal hypertension. Diagnosis:On CT, Cruveilhier-Baumgarten disease is characterized by the presence of a dilated tortuous paraumbilical vein in patients with cirrhosis, which arises from the left portal vein branch, traverses along the falciform ligament towards the umbilicus, forming a network of dilated periumbilical veins giving a "caput medusae" appearance. The blood eventually drains into the systemic circulation via the superficial and deep epigastric veins reaching the external iliac or femoral vein. Multidetector computed tomography (MDCT) is the imaging modality of choice which delineates this portosystemic collateral pathway with exceptional precision. The clinical relevance of this syndrome lies in the fact that unintended iatrogenic injury of these vessels can cause potentially life-threatening hemorrhage during abdominal surgeries or paracentesis.Treatment:Although portosystemic shunting and splenectomy have been implemented in the past to treat this condition, liver transplantation becomes the treatment of choice by re-establishing physiologic portal circulation and appropriate organ function.NOTE: The above information is educational purpose. The information provided herein should not be used during any medical emergency or for the diagnosis or treatment of any medical condition.DISCLAIMER: This information should not substitute for seeking responsible, professional medical care.

0 Comments

Submit a Comment

Your email address will not be published. Required fields are marked *

This site uses Akismet to reduce spam. Learn how your comment data is processed.

Cart Preview

Rate This:

[Total: 0    Average: 0/5]
ADHD Symptoms in Teens Linked to Intensive Social Media Use

ADHD Symptoms in Teens Linked to Intensive Social Media Use

A new study, published in the medical journal JAMA, finds that the more teenagers involved in social media, the higher their risk is to develop the symptoms of attention deficit hyperactivity disorder (ADHD). These symptoms may include inattention, hyperactivity,...

Your Blood Type Determines the Risk of Being Attacked by Ticks

Your Blood Type Determines the Risk of Being Attacked by Ticks

Scientists from the Check Republic discovered the evidence that ticks may prefer attacking people with a certain blood type. Tick, the blood-sucking parasites, can carry various bacteria, including bugs that cause the Lyme disease. In the course of study, the...

[WpProQuiz 1]

Featured Products

How to Choose the Right Sport for You?

We all know that doing sports is very important, both for health and for a beautiful body. But at the moment when we decide to finally take the path, we are faced with the question: what kind of sport is right for me? So, let's start with the fact that a lot of people...

read more