Periosteal desmoid tumor
Periosteal desmoid tumor
Description, Causes and Risk Factors:
Periosteal desmoid is a tumor-like fibrous proliferation of the periosteum at the musculotendinous attachment of the adductor magnus or the medial head of the gastrocnemius muscle on the posteromedial cortex of the distal femur. Because of its location, it also goes by the following names: distal metaphyseal femoral defect or medial supracondylar defect of the femur.
The etiology is thought to be related to repetitive trauma, similar to tug lesions elsewhere in the body. It is, therefore, also called an avulsive cortical irregularity. Although the term periosteal desmoid is widely accepted, it has an unfortunate similarity to the term desmoid tumor of soft tissue.
Periosteal desmoid usually occurs between the ages of 12 and 20 years, mainly in boys. There is no significant racial or ethnic distribution.
In the United States, approximately 900 people are diagnosed with periosteal desmoid tumors every year.
Difficulty in walking and doing regular activities.
Local pain and tenderness around the knee.
Blood test includes hemoglobin (Hb/Hgb) level, white blood cells (WBCs), erythrocyte sedimentation rate (ESR), and serum biochemistry.
Radiographic findings include a saucer-like cortical defect at the posteromedial cortex of the distal femur. The base is usually sclerotic, but may be poorly defined and irregular. Small bony spicules at the cortical surface may simulate an aggressive lesion.
Scintigraphy is usually normal, but focal increase in activity can occasionally be seen.
MRI reveals a T1-hypointense, T2-hyperintense lesion with a hypointense base at or near the attachment of the adductor magnus or medial head of the gastrocnemius muscles. Periosseous and marrow edema may also be seen.
Histopathologic examination of the lesion demonstrate fibroblastic spindle cells that produces large amount of collagen.
If you are diagnosed with a desmoid tumor it is recommended that you be evaluated in a major academic hospital. Patients with periosteal desmoid tumors should be evaluated by an orthopedist and oncologist. In more severe cases Multidisciplinary approach is indicated. Surgery followed by radiation and medical therapy is the most commonly used treatment is majority of cases.
NOTE: The above information is educational purpose. The information provided herein should not be used during any medical emergency or for the diagnosis or treatment of any medical condition.
DISCLAIMER: This information should not substitute for seeking responsible, professional medical care.
It is time for us to find the solution how to deal with extra weight which is coming with Christmas and New Year’s celebrations because 2018 is almost over and 2019 is getting closer. The main aim is obviously staying in shape and today will find an effective way to...
A study, recently published in the European Heart Journal, suggests that excessive sleep, as well as insufficient sleep, may cause the risk of cardiovascular issues and premature death. For the study, the researchers examined the sleeping habits of more than 116,000...
It is time for us to find the solution how to deal with extra weight which is coming with Christmas and New Year’s celebrations because 2018 is almost over and 2019 is getting closer. The main aim is obviously staying in shape and today will find an effective way to...read more
We know that moderate exercise strengthens our health and makes us more beautiful. But few know about the importance of doing sports as psychotherapy. And, nevertheless, physical loads can save from depressions, reduce anxiety, relieve from professional burnout,...read more
Factors such as age, gender, physical activity, genetics, medical history, body type, and others directly affect not only the desire to lose weight, but also to follow the right diet. Everything is relative, everything is individual. Nevertheless, there are universal...read more